作者：李东坤，温华知，张天成，王静静 ，刘晓楷，刘澳回

单位：

1.730000甘肃省兰州市，甘肃中医药大学第一临床医 学院　 2.730000甘肃省兰州市，甘肃省人民医院心内一科

Units：

1.First School of Clinical Medical of Gansu University of Chinese Medicine, Lanzhou 730000, China 2.Department of Cardiovascular Medicine, Gansu Provincial Hospital, Lanzhou 730000, China

关键词：

肺动脉高压；纵隔炎；房间隔缺损；病例报告

Keywords：

Pulmonary arterial hypertension; Mediastinitis; Heart septal defects, atrial; Case reports

CLC：

R 7541.5 R 564.2

DOI：

10.12114/j.issn.1008-5971.2023.00.189

Funds：

国家自然科学基金资助项目（81360038）

摘要：

纤维性纵隔炎是一种少见的由纤维组织逐渐取代纵隔脂肪组织的良性疾病。由于纤维性纵隔炎较为少 见，其导致的肺动脉高压及右心衰竭易被漏诊和误诊。本文报道1例纤维性纵隔炎伴房间隔缺损致肺动脉高压患者， 其于肺静脉植入1枚支架后症状好转。

Abstract：

Fibrous mediastinitis is a rare benign disease in which fibrous tissue gradually replaces mediastinal adipose tissue. Because fibrous mediastinitis is rare, the pulmonary arterial hypertension and right heart failure caused by it is easy to be missed and misdiagnosed. This paper reports a case of pulmonary arterial hypertension caused by fibrous mediastinitis with atrial septal defect. A stent was implanted in pulmonary vein, and the patient's symptoms improved.

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