作者：武倩文，孙晓萱，王嫱

单位：

210029江苏省南京市，江苏省人民医院 南京医科大学第一附属医院风湿免疫科

Units：

Departments of Rheumatology, Jiangsu Province Hospital/Nanjing Medical University First Affiliated Hospital, Nanjing 210029, China

关键词：

结缔组织病；肺动脉高压；结缔组织病相关肺动脉高压；心室功能，右；超声心动描记术；心脏磁共振；心电描记术；综述

Keywords：

Connective tissue diseases; Pulmonary arterial hypertension; Connective tissue disease associated with pulmonary arterial hypertension; Ventricular function, right; Echocardiography; Cardiac magnetic resonance; Electrocardiography;Review

CLC：

DOI：

10.12114/j.issn.1008-5971.2022.00.175

Funds：

国家自然科学基金资助项目（81701610）

摘要：

肺动脉高压（PAH）是结缔组织病（CTD）严重并发症之一，是CTD患者死亡的独立危险因素。右心室功能不全是结缔组织病相关肺动脉高压（CTD-PAH）预后不良的主要原因。无创影像学检查方法对CTD-PAH患者右心室功能的评估至关重要，起到预测疾病预后及指导治疗的作用。本文旨在对无创影像学方法评估CTD-PAH患者右心室功能的最新研究进行总结，以期为CTD-PAH患者右心室功能评估方法的选择提供参考。

Abstract：

Pulmonary arterial hypertension (PAH) is one of the serious complications of connective tissue diseases(CTD) and an independent risk factor for death in CTD patients. Right ventricle dysfunction is the main cause of poor prognosisin connective tissue disease associated with pulmonary arterial hypertension (CTD-PAH) . Noninvasive imaging examination isvery important for right ventricular function in patients with CTD-PAH, which can predict prognosis and guide treatment. Thispaper aims to summarize and review the research progress of noninvasive imaging methods for right ventricular function of patientswithCTD-PAH, in order to provide a reference for the selection of right ventricular function assessment methods for CTD-PAHpatients.

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